Statements (33)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:protein
gptkb:serine_protease |
| gptkbp:administeredBy |
intravenous injection
|
| gptkbp:alternativeName |
gptkb:C1_esterase_inhibitor
gptkb:C1INH |
| gptkbp:approvedBy |
gptkb:FDA
|
| gptkbp:deficiencyCauses |
gptkb:hereditary_hemorrhagic_telangiectasia
|
| gptkbp:encodedBy |
gptkb:SERPING1_gene
|
| gptkbp:foundIn |
human plasma
|
| gptkbp:glycosylation |
heavily glycosylated
|
| gptkbp:inhibitedBy |
gptkb:MASP-1
gptkb:MASP-2 gptkb:C1r gptkb:C1s gptkb:coagulation_factor_XIa gptkb:kallikrein gptkb:factor_XIIa plasmin |
| gptkbp:locatedOnChromosome |
gptkb:chromosome_11q12-q13.1
|
| gptkbp:medicalUse |
treatment of hereditary angioedema
|
| gptkbp:molecularWeight |
~105 kDa
|
| gptkbp:OMIM |
606860
|
| gptkbp:producedBy |
liver
|
| gptkbp:regulates |
gptkb:coagulation_system
gptkb:fibrinolytic_system complement system contact system |
| gptkbp:structure |
gptkb:protein
|
| gptkbp:UniProtID |
P05155
|
| gptkbp:usedAs |
gptkb:therapeutic_agent
|
| gptkbp:bfsParent |
gptkb:FXI
|
| gptkbp:bfsLayer |
7
|
| https://www.w3.org/2000/01/rdf-schema#label |
C1-inhibitor
|