pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial
GPTKB entity
Statements (18)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:protein
|
| gptkbp:alternativeName |
E1 alpha 1
PDHA1 protein |
| gptkbp:associatedWith |
gptkb:pyruvate_dehydrogenase_E1-alpha_deficiency
|
| gptkbp:biologicalProcess |
thiamine pyrophosphate binding
|
| gptkbp:EC_number |
1.2.4.1
|
| gptkbp:encodedBy |
PDHA1 gene
|
| gptkbp:function |
catalyzes decarboxylation of pyruvate
links glycolysis to citric acid cycle |
| gptkbp:locatedIn |
mitochondrion
|
| gptkbp:locatedOnChromosome |
Xq13.1
|
| gptkbp:organism |
gptkb:Homo_sapiens
|
| gptkbp:partOf |
gptkb:pyruvate_dehydrogenase_complex
|
| gptkbp:subunit |
pyruvate dehydrogenase E1 enzyme
|
| gptkbp:UniProtID |
gptkb:P08559
|
| gptkbp:bfsParent |
gptkb:PDHA1
|
| gptkbp:bfsLayer |
8
|
| https://www.w3.org/2000/01/rdf-schema#label |
pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial
|