large cell neuroendocrine carcinoma

GPTKB entity

Statements (28)
Predicate Object
gptkbp:instanceOf gptkb:cancer
Neuroendocrine Tumor
gptkbp:affectsOrgan gptkb:cancer
gastrointestinal tract
bladder
gptkbp:canMetastasizeTo common at diagnosis
gptkbp:differentialDiagnosis gptkb:small_cell_lung_carcinoma
gptkb:large_cell_carcinoma
atypical carcinoid
gptkbp:firstDescribed 1991
gptkbp:histology large cells with neuroendocrine features
https://www.w3.org/2000/01/rdf-schema#label large cell neuroendocrine carcinoma
gptkbp:ICD-10_code C34
gptkbp:incidence rare
gptkbp:marking gptkb:chromogranin_A
gptkb:CD56
synaptophysin
gptkbp:mutationAssociatedWith gptkb:RB1
gptkb:TP53
gptkbp:prognosis poor
gptkbp:subspecies extrapulmonary large cell neuroendocrine carcinoma
pulmonary large cell neuroendocrine carcinoma
gptkbp:treatment surgery
radiation therapy
chemotherapy
gptkbp:WHOClassification high-grade neuroendocrine carcinoma
gptkbp:bfsParent gptkb:large_cell_carcinoma
gptkbp:bfsLayer 6