Statements (22)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:enzyme
|
gptkbp:alternativeName |
gptkb:IDS
gptkb:iduronate_2-sulfatase gptkb:arylsulfatase_B |
gptkbp:associatedWith |
gptkb:Mucopolysaccharidosis_type_II
|
gptkbp:biologicalProcess |
hydrolase activity
|
gptkbp:CASNumber |
9028-83-1
|
gptkbp:deficiencyCauses |
gptkb:Hunter_syndrome
|
gptkbp:EC_number |
3.1.6.13
|
gptkbp:function |
removes sulfate groups from dermatan sulfate and heparan sulfate
|
gptkbp:gene |
gptkb:IDS
|
https://www.w3.org/2000/01/rdf-schema#label |
iduronate-2-sulfatase
|
gptkbp:locatedOnChromosome |
gptkb:Xq28
|
gptkbp:location |
gptkb:lysosome
|
gptkbp:OMIM |
300823
|
gptkbp:proteinFamily |
sulfatase family
|
gptkbp:species |
gptkb:Homo_sapiens
|
gptkbp:substrate |
dermatan sulfate
heparan sulfate |
gptkbp:UniProtID |
P22304
|
gptkbp:bfsParent |
gptkb:MPS_II
|
gptkbp:bfsLayer |
6
|