Statements (28)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:enzyme
|
gptkbp:alternativeName |
gptkb:N-acetylgalactosamine-4-sulfatase
gptkb:ASB |
gptkbp:associatedWith |
gptkb:Maroteaux-Lamy_syndrome
|
gptkbp:biologicalProcess |
arylsulfatase activity
|
gptkbp:cellularComponent |
gptkb:lysosomal_lumen
|
gptkbp:deficiencyCauses |
gptkb:mucopolysaccharidosis_type_VI
|
gptkbp:EC_number |
3.1.6.12
|
gptkbp:encodedBy |
gptkb:ARSB_gene
|
gptkbp:Enzyme_Commission_category |
gptkb:hydrolase
|
gptkbp:foundIn |
gptkb:lysosome
|
gptkbp:function |
removes sulfate groups from glycosaminoglycans
|
gptkbp:gene |
gptkb:ARSB
|
gptkbp:HGNC_ID |
711
|
https://www.w3.org/2000/01/rdf-schema#label |
arylsulfatase B
|
gptkbp:locatedOnChromosome |
gptkb:5q14.1
|
gptkbp:OMIM |
611542
|
gptkbp:RefSeq |
NP_000037.2
|
gptkbp:substrate |
dermatan sulfate
chondroitin sulfate |
gptkbp:UniProtID |
gptkb:P15848
|
gptkbp:bfsParent |
gptkb:iduronate-2-sulfatase
gptkb:ARSB gptkb:MPS6 gptkb:Mucopolysaccharidosis_type_VI gptkb:ARSB_gene gptkb:Maroteaux-Lamy_syndrome |
gptkbp:bfsLayer |
7
|