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PSP-Richardson's syndrome
URI:
https://gptkb.org/entity/PSP-Richardson's_syndrome
GPTKB entity
Statements (39)
Predicate
Object
gptkbp:instanceOf
gptkb:atypical_parkinsonism
neurodegenerative disease
gptkbp:affects
gptkb:basal_ganglia
brainstem
midbrain
gptkbp:alsoKnownAs
Progressive Supranuclear Palsy - Richardson's syndrome
gptkbp:causedBy
tau protein accumulation
gptkbp:diagnosedBy
MRI
clinical criteria
gptkbp:differentialDiagnosis
gptkb:Parkinson's_disease
gptkb:corticobasal_degeneration
gptkb:multiple_system_atrophy
gptkbp:firstDescribed
1963
J. Clifford Richardson
https://www.w3.org/2000/01/rdf-schema#label
PSP-Richardson's syndrome
gptkbp:ICD-10_code
G23.1
gptkbp:mortalityRate
high
gptkbp:OMIM
601104
gptkbp:onset
late adulthood
gptkbp:partOf
Progressive Supranuclear Palsy (PSP)
gptkbp:prevalence
rare
gptkbp:prognosis
progressive
poor
gptkbp:relatedTo
gptkb:PSP-parkinsonism
PSP-pure akinesia with gait freezing
gptkbp:riskFactor
age
genetic predisposition
gptkbp:symptom
bradykinesia
postural instability
cognitive impairment
dysphagia
dysarthria
vertical gaze palsy
axial rigidity
gptkbp:treatment
supportive care
physical therapy
speech therapy
gptkbp:bfsParent
gptkb:Progressive_Supranuclear_Palsy
gptkbp:bfsLayer
7