Statements (29)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:leukemia
gptkb:disease |
| gptkbp:affects |
gptkb:natural_killer_cells
|
| gptkbp:causedBy |
gptkb:unknown
|
| gptkbp:diagnosedBy |
bone marrow biopsy
immunophenotyping peripheral blood smear flow cytometry |
| gptkbp:hasMedianAgeOfOnset |
middle-aged adults
|
| gptkbp:hasOrphanetID |
ORPHA:98256
|
| gptkbp:hasSexRatio |
slight male predominance
|
| gptkbp:ICD-10_code |
C91.6
|
| gptkbp:prevalence |
rare
|
| gptkbp:prognosis |
variable
|
| gptkbp:subclassOf |
gptkb:large_granular_lymphocyte_leukemia
|
| gptkbp:symptom |
autoimmune disorders
fatigue splenomegaly recurrent infections cytopenia |
| gptkbp:synonym |
gptkb:Natural_killer_cell_large_granular_lymphocyte_leukemia
|
| gptkbp:treatment |
gptkb:cyclophosphamide
gptkb:cyclosporine gptkb:methotrexate chemotherapy immunosuppressive therapy |
| gptkbp:bfsParent |
gptkb:LGL_Leukemia
|
| gptkbp:bfsLayer |
7
|
| https://www.w3.org/2000/01/rdf-schema#label |
NK-cell LGL Leukemia
|