Churg-Strauss syndrome

GPTKB entity

Statements (53)
Predicate Object
gptkbp:instanceOf gptkb:disease
gptkb:vasculitis
gptkbp:abbreviation gptkb:EGPA
gptkbp:affects adults
both sexes
medium blood vessels
small blood vessels
gptkbp:alsoKnownAs gptkb:eosinophilic_granulomatosis_with_polyangiitis
gptkbp:autoantibody ANCA (antineutrophil cytoplasmic antibody)
gptkbp:category gptkb:autoimmune_disease
gptkb:systemic_vasculitis
gptkbp:cause gptkb:unknown
gptkbp:characterizedBy gptkb:vasculitis
asthma
granulomatous inflammation
eosinophilia
gptkbp:complication gptkb:peripheral_neuropathy
heart failure
renal failure
gastrointestinal bleeding
gptkbp:diagnosedBy gptkb:blood_test
clinical criteria
biopsy
imaging studies
gptkbp:firstDescribed gptkb:Jacob_Churg
gptkb:Lotte_Strauss
1951
gptkbp:ICD-10_code M30.1
gptkbp:prevalence rare
gptkbp:prognosis variable
gptkbp:relatedTo gptkb:granulomatosis_with_polyangiitis
microscopic polyangiitis
gptkbp:riskFactor allergic rhinitis
history of asthma
gptkbp:symptom gptkb:sinusitis
gptkb:peripheral_neuropathy
asthma
fever
abdominal pain
joint pain
muscle pain
weight loss
skin rash
cardiac involvement
gptkbp:treatment corticosteroids
immunosuppressive drugs
biologic agents
gptkbp:bfsParent gptkb:EGPA
gptkb:Granulomatosis_with_polyangiitis
gptkb:eosinophilic_granulomatosis_with_polyangiitis
gptkb:eosinophils
gptkbp:bfsLayer 7
https://www.w3.org/2000/01/rdf-schema#label Churg-Strauss syndrome