Statements (53)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:disease
vasculitis |
gptkbp:abbreviation |
gptkb:EGPA
|
gptkbp:affects |
adults
both sexes medium blood vessels small blood vessels |
gptkbp:alsoKnownAs |
gptkb:eosinophilic_granulomatosis_with_polyangiitis
|
gptkbp:autoantibody |
ANCA (antineutrophil cytoplasmic antibody)
|
gptkbp:category |
autoimmune disease
systemic vasculitis |
gptkbp:cause |
unknown
|
gptkbp:characterizedBy |
asthma
vasculitis granulomatous inflammation eosinophilia |
gptkbp:complication |
heart failure
renal failure gastrointestinal bleeding peripheral neuropathy |
gptkbp:diagnosedBy |
blood test
clinical criteria biopsy imaging studies |
gptkbp:firstDescribed |
gptkb:Jacob_Churg
gptkb:Lotte_Strauss 1951 |
https://www.w3.org/2000/01/rdf-schema#label |
Churg-Strauss syndrome
|
gptkbp:ICD-10_code |
M30.1
|
gptkbp:prevalence |
rare
|
gptkbp:prognosis |
variable
|
gptkbp:relatedTo |
gptkb:granulomatosis_with_polyangiitis
microscopic polyangiitis |
gptkbp:riskFactor |
allergic rhinitis
history of asthma |
gptkbp:symptom |
gptkb:sinusitis
asthma fever abdominal pain joint pain muscle pain weight loss peripheral neuropathy skin rash cardiac involvement |
gptkbp:treatment |
corticosteroids
immunosuppressive drugs biologic agents |
gptkbp:bfsParent |
gptkb:EGPA
gptkb:Granulomatosis_with_polyangiitis gptkb:eosinophilic_granulomatosis_with_polyangiitis gptkb:eosinophils |
gptkbp:bfsLayer |
7
|