EGPA

GPTKB entity

Statements (41)
Predicate Object
gptkbp:instanceOf gptkb:disease
vasculitis
gptkbp:affects gptkb:nervous_system
heart
gastrointestinal tract
kidneys
small blood vessels
gptkbp:associatedWith peripheral neuropathy
allergic rhinitis
skin lesions
lung infiltrates
gptkbp:characterizedBy asthma
vasculitis
granulomatous inflammation
eosinophilia
gptkbp:diagnosedBy biopsy
ANCA test
blood eosinophil count
gptkbp:firstDescribed gptkb:Jacob_Churg
gptkb:Lotte_Strauss
1951
gptkbp:formerName gptkb:Churg-Strauss_syndrome
gptkbp:fullName gptkb:Eosinophilic_Granulomatosis_with_Polyangiitis
gptkbp:hasOrphanetID ORPHA:911
https://www.w3.org/2000/01/rdf-schema#label EGPA
gptkbp:ICD-10_code M30.1
gptkbp:isANCAAssociatedVasculitis true
gptkbp:isAutoimmune true
gptkbp:mortalityRate low with treatment
gptkbp:OMIM 600334
gptkbp:prevalence rare
gptkbp:prognosis variable
gptkbp:symptom fever
joint pain
muscle pain
weight loss
gptkbp:treatment biologics
corticosteroids
immunosuppressants
gptkbp:bfsParent gptkb:Kirkwall_Airport
gptkbp:bfsLayer 6