eosinophilic granulomatosis with polyangiitis

GPTKB entity

Statements (40)
Predicate Object
gptkbp:instanceOf gptkb:disease
autoimmune disease
vasculitis
gptkbp:affects gptkb:skin
heart
lungs
kidneys
blood vessels
nerves
gptkbp:alsoKnownAs gptkb:Churg-Strauss_syndrome
gptkbp:associatedWith gptkb:ANCA_antibodies
gptkbp:cause unknown
gptkbp:diagnosedBy imaging
blood test
biopsy
gptkbp:firstDescribed gptkb:Jacob_Churg
gptkb:Lotte_Strauss
1951
https://www.w3.org/2000/01/rdf-schema#label eosinophilic granulomatosis with polyangiitis
gptkbp:ICD-10_code M30.1
gptkbp:mortalityRate variable
gptkbp:period eosinophilic phase
prodromal phase
vasculitic phase
gptkbp:prevalence rare
gptkbp:prognosis improves with treatment
gptkbp:riskFactor allergic rhinitis
history of asthma
gptkbp:symptom gptkb:sinusitis
asthma
fever
peripheral neuropathy
skin rash
eosinophilia
gptkbp:treatment biologics
corticosteroids
immunosuppressants
gptkbp:bfsParent gptkb:antineutrophil_cytoplasmic_antibodies
gptkb:Eosinophil-associated_syndrome
gptkbp:bfsLayer 6