gptkbp:instanceOf
|
gptkb:disease
|
gptkbp:affects
|
humans
central nervous system
|
gptkbp:averageSurvival
|
less than 1 year
|
gptkbp:casualties
|
yes
|
gptkbp:category
|
gptkb:transmissible_spongiform_encephalopathy
neurodegenerative disease
|
gptkbp:cause
|
spongiform changes in brain tissue
|
gptkbp:causedBy
|
prion
|
gptkbp:diagnosedBy
|
gptkb:EEG
MRI
CSF test
|
gptkbp:firstDescribed
|
1920
|
gptkbp:fullName
|
gptkb:Creutzfeldt–Jakob_disease
|
https://www.w3.org/2000/01/rdf-schema#label
|
CJD
|
gptkbp:ICD-10_code
|
A81.0
|
gptkbp:MeSH_ID
|
D003456
|
gptkbp:namedAfter
|
gptkb:Alfons_Maria_Jakob
gptkb:Hans_Gerhard_Creutzfeldt
|
gptkbp:notifiableDisease
|
yes
|
gptkbp:OMIM
|
123400
|
gptkbp:prevalence
|
1 in 1 million per year
|
gptkbp:prognosis
|
poor
|
gptkbp:relatedTo
|
gptkb:Gerstmann–Sträussler–Scheinker_syndrome
gptkb:fatal_familial_insomnia
kuru
|
gptkbp:subspecies
|
gptkb:familial_CJD
gptkb:iatrogenic_CJD
gptkb:sporadic_CJD
gptkb:variant_CJD
|
gptkbp:symptom
|
gptkb:dementia
memory loss
muscle stiffness
involuntary movements
personality changes
|
gptkbp:transmission
|
hereditary
sporadic
iatrogenic
variant (vCJD)
|
gptkbp:treatment
|
no cure
|
gptkbp:bfsParent
|
gptkb:Creutzfeldt-Jakob_disease
|
gptkbp:bfsLayer
|
6
|