Statements (32)
Predicate | Object |
---|---|
gptkbp:instanceOf |
neurodegenerative disease
prion disease |
gptkbp:affects |
humans
|
gptkbp:alsoKnownAs |
gptkb:vCJD
|
gptkbp:casualties |
yes
|
gptkbp:causedBy |
prion
|
gptkbp:diagnosedBy |
MRI
brain biopsy cerebrospinal fluid test |
gptkbp:differentialDiagnosis |
gptkb:Alzheimer's_disease
gptkb:sporadic_CJD gptkb:Huntington's_disease |
gptkbp:firstDescribed |
1996
|
gptkbp:hasEpidemiology |
mainly UK
|
gptkbp:hasNoCure |
true
|
https://www.w3.org/2000/01/rdf-schema#label |
variant CJD
|
gptkbp:ICD-10_code |
A81.0
|
gptkbp:medianSurvival |
13-14 months
|
gptkbp:MeSH_ID |
D020868
|
gptkbp:OMIM |
123400
|
gptkbp:prevention |
food safety measures
blood donation restrictions |
gptkbp:prognosis |
poor
|
gptkbp:relatedTo |
gptkb:bovine_spongiform_encephalopathy
|
gptkbp:symptom |
gptkb:dementia
ataxia psychiatric symptoms sensory disturbances |
gptkbp:transmission |
blood transfusion
consumption of BSE-contaminated beef |
gptkbp:bfsParent |
gptkb:Creutzfeldt–Jakob_disease
|
gptkbp:bfsLayer |
6
|