splenic marginal zone lymphoma

GPTKB entity

Statements (30)
Predicate Object
gptkbp:instanceOf leukemia
gptkbp:affects blood
spleen
bone marrow
gptkbp:alternativeName SMZL
splenic small B-cell lymphoma
gptkbp:associatedWith 7q deletion
KLF2 mutation
NOTCH2 mutation
gptkbp:hasOrphanetID ORPHA:52460
gptkbp:hasRelapseRisk moderate
https://www.w3.org/2000/01/rdf-schema#label splenic marginal zone lymphoma
gptkbp:ICD-10_code C88.4
gptkbp:medianAge 65
gptkbp:MeSH_ID D054198
gptkbp:originatedIn gptkb:B_cell
gptkbp:prognosis indolent
gptkbp:rarity true
gptkbp:subclassOf gptkb:marginal_zone_lymphoma
gptkbp:symptom gptkb:anemia
fatigue
splenomegaly
thrombocytopenia
lymphocytosis
gptkbp:treatment gptkb:rituximab
gptkb:splenectomy
chemotherapy
immunotherapy
gptkbp:bfsParent gptkb:marginal_zone_lymphoma
gptkbp:bfsLayer 7