splenic marginal zone lymphoma
GPTKB entity
Statements (30)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:leukemia
|
| gptkbp:affects |
blood
spleen bone marrow |
| gptkbp:alternativeName |
SMZL
splenic small B-cell lymphoma |
| gptkbp:associatedWith |
7q deletion
KLF2 mutation NOTCH2 mutation |
| gptkbp:hasOrphanetID |
ORPHA:52460
|
| gptkbp:hasRelapseRisk |
moderate
|
| gptkbp:ICD-10_code |
C88.4
|
| gptkbp:medianAge |
65
|
| gptkbp:MeSH_ID |
D054198
|
| gptkbp:originatedIn |
gptkb:B_cell
|
| gptkbp:prognosis |
indolent
|
| gptkbp:rarity |
true
|
| gptkbp:subclassOf |
gptkb:marginal_zone_lymphoma
|
| gptkbp:symptom |
gptkb:anemia
fatigue splenomegaly thrombocytopenia lymphocytosis |
| gptkbp:treatment |
gptkb:rituximab
gptkb:immunotherapy gptkb:splenectomy chemotherapy |
| gptkbp:bfsParent |
gptkb:marginal_zone_lymphoma
|
| gptkbp:bfsLayer |
8
|
| https://www.w3.org/2000/01/rdf-schema#label |
splenic marginal zone lymphoma
|