splenic marginal zone lymphoma
GPTKB entity
Statements (30)
Predicate | Object |
---|---|
gptkbp:instanceOf |
leukemia
|
gptkbp:affects |
blood
spleen bone marrow |
gptkbp:alternativeName |
SMZL
splenic small B-cell lymphoma |
gptkbp:associatedWith |
7q deletion
KLF2 mutation NOTCH2 mutation |
gptkbp:hasOrphanetID |
ORPHA:52460
|
gptkbp:hasRelapseRisk |
moderate
|
https://www.w3.org/2000/01/rdf-schema#label |
splenic marginal zone lymphoma
|
gptkbp:ICD-10_code |
C88.4
|
gptkbp:medianAge |
65
|
gptkbp:MeSH_ID |
D054198
|
gptkbp:originatedIn |
gptkb:B_cell
|
gptkbp:prognosis |
indolent
|
gptkbp:rarity |
true
|
gptkbp:subclassOf |
gptkb:marginal_zone_lymphoma
|
gptkbp:symptom |
gptkb:anemia
fatigue splenomegaly thrombocytopenia lymphocytosis |
gptkbp:treatment |
gptkb:rituximab
gptkb:splenectomy chemotherapy immunotherapy |
gptkbp:bfsParent |
gptkb:marginal_zone_lymphoma
|
gptkbp:bfsLayer |
7
|