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primary mediastinal B-lymphoma
URI:
https://gptkb.org/entity/primary_mediastinal_B-lymphoma
GPTKB entity
Statements (31)
Predicate
Object
gptkbp:instanceOf
gptkb:leukemia
gptkb:disease
gptkbp:abbreviation
gptkb:PMBCL
gptkbp:differentialDiagnosis
gptkb:germ_cell_tumor
gptkb:classical_Hodgkin_lymphoma
thymoma
gptkbp:hasGeneticFeature
frequent 9p24.1 amplification
gptkbp:hasImmunophenotype
CD30 positive
CD20 positive
BCL6 variable
CD10 negative
CD23 positive
MUM1 positive
gptkbp:hasLocation
gptkb:mediastinum
gptkbp:hasTypicalAgeOfOnset
young adult
gptkbp:hasTypicalSexDistribution
female predominance
gptkbp:ICD-10_code
C85.2
gptkbp:originatedIn
B-cell
gptkbp:prognosis
generally favorable with modern therapy
gptkbp:subclassOf
diffuse large B-cell lymphoma
gptkbp:symptom
gptkb:superior_vena_cava_syndrome
cough
dyspnea
chest mass
gptkbp:synonym
gptkb:primary_mediastinal_large_B-cell_lymphoma
gptkbp:treatment
gptkb:radiation_therapy
gptkb:immunotherapy
chemotherapy
gptkbp:bfsParent
gptkb:primary_mediastinal_large_B-cell_lymphoma
gptkbp:bfsLayer
8
https://www.w3.org/2000/01/rdf-schema#label
primary mediastinal B-lymphoma