methylmalonyl-CoA mutase

GPTKB entity

Statements (22)
Predicate Object
gptkbp:instanceOf gptkb:enzyme
gptkbp:alternativeName gptkb:MCM
methylmalonyl coenzyme A mutase
gptkbp:CASNumber 9023-90-1
gptkbp:catalyzes conversion of methylmalonyl-CoA to succinyl-CoA
gptkbp:cofactor adenosylcobalamin
gptkbp:deficiencyCauses methylmalonic acidemia
gptkbp:EC_number 5.4.99.2
gptkbp:foundIn mitochondria
gptkbp:gene gptkb:MUT
https://www.w3.org/2000/01/rdf-schema#label methylmalonyl-CoA mutase
gptkbp:involves propionate metabolism
gptkbp:OMIM 609058
gptkbp:organism gptkb:Homo_sapiens
gptkbp:PDB 2XIQ
gptkbp:product gptkb:succinyl-CoA
gptkbp:requires vitamin B12
gptkbp:structure homodimer
gptkbp:substrate L-methylmalonyl-CoA
gptkbp:UniProtID P22033
gptkbp:bfsParent gptkb:TIM_barrel
gptkbp:bfsLayer 8