Statements (22)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:enzyme
|
| gptkbp:alternativeName |
gptkb:MCM
methylmalonyl coenzyme A mutase |
| gptkbp:CASNumber |
9023-90-1
|
| gptkbp:catalyzes |
conversion of methylmalonyl-CoA to succinyl-CoA
|
| gptkbp:cofactor |
adenosylcobalamin
|
| gptkbp:deficiencyCauses |
methylmalonic acidemia
|
| gptkbp:EC_number |
5.4.99.2
|
| gptkbp:foundIn |
mitochondria
|
| gptkbp:gene |
gptkb:MUT
|
| gptkbp:involves |
propionate metabolism
|
| gptkbp:OMIM |
609058
|
| gptkbp:organism |
gptkb:Homo_sapiens
|
| gptkbp:PDB |
2XIQ
|
| gptkbp:product |
gptkb:succinyl-CoA
|
| gptkbp:requires |
vitamin B12
|
| gptkbp:structure |
homodimer
|
| gptkbp:substrate |
L-methylmalonyl-CoA
|
| gptkbp:UniProtID |
P22033
|
| gptkbp:bfsParent |
gptkb:TIM_barrel
|
| gptkbp:bfsLayer |
8
|
| http://www.w3.org/2000/01/rdf-schema#label |
methylmalonyl-CoA mutase
|