Statements (33)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:disease
rare cancer |
| gptkbp:affects |
humans
|
| gptkbp:canMetastasizeTo |
true
|
| gptkbp:differentialDiagnosis |
gptkb:systemic_mastocytosis
other sarcomas |
| gptkbp:firstDescribed |
1986
|
| gptkbp:hasGeneticAlteration |
KIT mutation
|
| gptkbp:hasImmunohistochemistryMarker |
gptkb:CD117
gptkb:CD25 tryptase |
| gptkbp:hasMalignancy |
malignant
|
| gptkbp:histology |
atypical mast cells
|
| https://www.w3.org/2000/01/rdf-schema#label |
mast cell sarcoma
|
| gptkbp:ICD-10_code |
C96.2
|
| gptkbp:incidence |
extremely rare
|
| gptkbp:isNotAssociatedWith |
systemic mastocytosis (in most cases)
|
| gptkbp:location |
gptkb:bone
gptkb:skin gastrointestinal tract lymph node soft tissue |
| gptkbp:mortalityRate |
high
|
| gptkbp:originatedIn |
mast cell
|
| gptkbp:prognosis |
poor
|
| gptkbp:symptom |
pain
swelling mass effect |
| gptkbp:treatment |
surgery
radiation therapy chemotherapy |
| gptkbp:bfsParent |
gptkb:mastocytosis
|
| gptkbp:bfsLayer |
8
|