idiopathic hypereosinophilic syndrome
GPTKB entity
Statements (41)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:disease
syndrome |
| gptkbp:affects |
gptkb:skin
gptkb:nervous_system lungs gastrointestinal tract cardiac system hematologic system |
| gptkbp:causedBy |
unknown
|
| gptkbp:complication |
heart failure
fibrosis thromboembolism |
| gptkbp:firstDescribed |
1968
|
| gptkbp:hasDiagnosticCriteria |
persistent eosinophilia >1500/μL for more than 6 months
absence of identifiable cause evidence of organ involvement |
| gptkbp:hasOrphanetID |
gptkb:ORPHA:324
|
| https://www.w3.org/2000/01/rdf-schema#label |
idiopathic hypereosinophilic syndrome
|
| gptkbp:ICD-10_code |
gptkb:D72.1
|
| gptkbp:inheritance |
sporadic
|
| gptkbp:MeSH_ID |
gptkb:D006967
|
| gptkbp:mortalityRate |
can be fatal if untreated
|
| gptkbp:prevalence |
rare
|
| gptkbp:prognosis |
variable
|
| gptkbp:symptom |
fever
fatigue weight loss cough shortness of breath skin rash neurological symptoms eosinophilia cardiac involvement |
| gptkbp:synonym |
gptkb:HES
idiopathic HES |
| gptkbp:treatment |
gptkb:interferon-alpha
gptkb:hydroxyurea gptkb:imatinib corticosteroids |
| gptkbp:bfsParent |
gptkb:PDGFRα
|
| gptkbp:bfsLayer |
6
|