alpha-galactosidase

GPTKB entity

Statements (28)
Predicate Object
gptkbp:instanceOf gptkb:enzyme
gptkbp:alternativeName alpha-D-galactoside galactohydrolase
melibiase
gptkbp:CASNumber 9025-35-8
gptkbp:catalyzes hydrolysis of terminal alpha-galactosyl moieties
gptkbp:deficiencyCauses gptkb:Fabry_disease
gptkbp:EC_number 3.2.1.22
gptkbp:foundIn gptkb:Bacteria
humans
plants
gptkbp:gene_encoding_in_humans gptkb:GLA
https://www.w3.org/2000/01/rdf-schema#label alpha-galactosidase
gptkbp:inhibitedBy galactose
gptkbp:molecularWeight ~46 kDa (human)
gptkbp:optimum_pH 37°C
4.5-6.0
gptkbp:PDB 1R46
gptkbp:presentIn lysosome (in humans)
gptkbp:substrate melibiose
raffinose
stachyose
gptkbp:used_in food industry
digestive aids
Beano (dietary supplement)
gptkbp:usedFor gptkb:Fabry_disease
gptkbp:bfsParent gptkb:MEL1
gptkb:EC_3.2.1.23
gptkbp:bfsLayer 8