Statements (28)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:enzyme
|
gptkbp:alternativeName |
alpha-D-galactoside galactohydrolase
melibiase |
gptkbp:CASNumber |
9025-35-8
|
gptkbp:catalyzes |
hydrolysis of terminal alpha-galactosyl moieties
|
gptkbp:deficiencyCauses |
gptkb:Fabry_disease
|
gptkbp:EC_number |
3.2.1.22
|
gptkbp:foundIn |
gptkb:Bacteria
humans plants |
gptkbp:gene_encoding_in_humans |
gptkb:GLA
|
https://www.w3.org/2000/01/rdf-schema#label |
alpha-galactosidase
|
gptkbp:inhibitedBy |
galactose
|
gptkbp:molecularWeight |
~46 kDa (human)
|
gptkbp:optimum_pH |
37°C
4.5-6.0 |
gptkbp:PDB |
1R46
|
gptkbp:presentIn |
lysosome (in humans)
|
gptkbp:substrate |
melibiose
raffinose stachyose |
gptkbp:used_in |
food industry
digestive aids Beano (dietary supplement) |
gptkbp:usedFor |
gptkb:Fabry_disease
|
gptkbp:bfsParent |
gptkb:MEL1
gptkb:EC_3.2.1.23 |
gptkbp:bfsLayer |
8
|