NK-cell large granular lymphocyte leukemia

GPTKB entity

Statements (30)
Predicate Object
gptkbp:instanceOf gptkb:disease
leukemia
lymphoproliferative disorder
gptkbp:affects gptkb:natural_killer_cells
blood
gptkbp:causedBy unknown
gptkbp:diagnosedBy bone marrow biopsy
blood smear
flow cytometry
gptkbp:hasGenderPrevalence slight male predominance
gptkbp:hasOrphanetID ORPHA:98256
gptkbp:hasTypicalAgeOfOnset adulthood
https://www.w3.org/2000/01/rdf-schema#label NK-cell large granular lymphocyte leukemia
gptkbp:ICD-10_code C91.6
gptkbp:originatedIn gptkb:NK_cells
large granular lymphocytes
gptkbp:prevalence rare
gptkbp:prognosis variable
gptkbp:symptom autoimmune disorders
fatigue
splenomegaly
recurrent infections
cytopenia
gptkbp:synonym chronic NK-cell leukemia
chronic NK-cell lymphoproliferative disorder
gptkbp:treatment chemotherapy
immunosuppressive therapy
corticosteroids
gptkbp:bfsParent gptkb:Large_Granular_Lymphocyte_Leukemia
gptkbp:bfsLayer 8