Statements (16)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:protein
|
| gptkbp:alternativeName |
gptkb:2-oxoisovalerate_dehydrogenase_subunit_alpha
gptkb:E1a |
| gptkbp:associatedWith |
gptkb:maple_syrup_urine_disease
|
| gptkbp:component |
gptkb:branched-chain_alpha-keto_acid_dehydrogenase_complex
|
| gptkbp:encodedBy |
gptkb:BCKDHA_gene
|
| gptkbp:formsComplexWith |
gptkb:BCKD_E1_beta_subunit
|
| gptkbp:function |
catalyzes decarboxylation of branched-chain alpha-keto acids
|
| gptkbp:locatedOnChromosome |
19q13.2
|
| gptkbp:location |
mitochondrial matrix
|
| gptkbp:molecularWeight |
45 kDa
|
| gptkbp:organism |
gptkb:Homo_sapiens
|
| gptkbp:UniProtID |
P12694
|
| gptkbp:bfsParent |
gptkb:BCKDHA
|
| gptkbp:bfsLayer |
7
|
| https://www.w3.org/2000/01/rdf-schema#label |
BCKD E1 alpha subunit
|