Statements (16)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:protein
|
gptkbp:alternativeName |
gptkb:2-oxoisovalerate_dehydrogenase_subunit_alpha
gptkb:E1a |
gptkbp:associatedWith |
gptkb:maple_syrup_urine_disease
|
gptkbp:component |
gptkb:branched-chain_alpha-keto_acid_dehydrogenase_complex
|
gptkbp:encodedBy |
gptkb:BCKDHA_gene
|
gptkbp:formsComplexWith |
gptkb:BCKD_E1_beta_subunit
|
gptkbp:function |
catalyzes decarboxylation of branched-chain alpha-keto acids
|
https://www.w3.org/2000/01/rdf-schema#label |
BCKD E1 alpha subunit
|
gptkbp:locatedOnChromosome |
19q13.2
|
gptkbp:location |
mitochondrial matrix
|
gptkbp:molecularWeight |
45 kDa
|
gptkbp:organism |
gptkb:Homo_sapiens
|
gptkbp:UniProtID |
P12694
|
gptkbp:bfsParent |
gptkb:BCKDHA
|
gptkbp:bfsLayer |
7
|