2-oxoisovalerate dehydrogenase subunit alpha
GPTKB entity
Statements (13)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:protein
|
| gptkbp:associatedWith |
gptkb:maple_syrup_urine_disease
|
| gptkbp:EC_number |
1.2.4.4
|
| gptkbp:foundIn |
mitochondria
|
| gptkbp:function |
catalyzes oxidative decarboxylation of 2-oxoisovalerate
|
| gptkbp:gene |
gptkb:BCKDHA
|
| gptkbp:involvedIn |
leucine catabolism
isoleucine catabolism valine catabolism |
| gptkbp:partOf |
gptkb:branched-chain_alpha-keto_acid_dehydrogenase_complex
|
| gptkbp:bfsParent |
gptkb:BCKD_E1_alpha_subunit
|
| gptkbp:bfsLayer |
8
|
| http://www.w3.org/2000/01/rdf-schema#label |
2-oxoisovalerate dehydrogenase subunit alpha
|