very-long-chain acyl-CoA dehydrogenase
GPTKB entity
Statements (21)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:enzyme
|
| gptkbp:alternativeName |
VLCAD
VLCAD enzyme |
| gptkbp:associatedWith |
very-long-chain acyl-CoA dehydrogenase deficiency
|
| gptkbp:cofactor |
gptkb:FAD
|
| gptkbp:EC_number |
1.3.8.9
|
| gptkbp:foundIn |
gptkb:Homo_sapiens
other mammals |
| gptkbp:function |
catalyzes the initial step of mitochondrial beta-oxidation of long-chain fatty acids
|
| gptkbp:gene |
gptkb:ACADVL
|
| https://www.w3.org/2000/01/rdf-schema#label |
very-long-chain acyl-CoA dehydrogenase
|
| gptkbp:locatedOnChromosome |
gptkb:chromosome_17p13.1
|
| gptkbp:location |
mitochondrial inner membrane
|
| gptkbp:molecularWeight |
~70 kDa
|
| gptkbp:OMIM |
609575
|
| gptkbp:product |
FADH2
trans-2,3-enoyl-CoA |
| gptkbp:substrate |
very-long-chain acyl-CoA
|
| gptkbp:UniProtID |
P49748
|
| gptkbp:bfsParent |
gptkb:acyl-CoA_dehydrogenase
|
| gptkbp:bfsLayer |
7
|