Statements (38)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:skin
autoimmune disease |
gptkbp:affects |
gptkb:skin
mucous membranes |
gptkbp:antibodyTarget |
gptkb:desmoglein_1
gptkb:desmoglein_3 |
gptkbp:causedBy |
autoantibodies
|
gptkbp:complication |
infection
dehydration |
gptkbp:diagnosedBy |
gptkb:ELISA
biopsy direct immunofluorescence |
gptkbp:differentialDiagnosis |
gptkb:bullous_pemphigoid
gptkb:mucous_membrane_pemphigoid gptkb:lichen_planus |
gptkbp:field |
immunology
dermatology |
gptkbp:firstDescribed |
1788
|
https://www.w3.org/2000/01/rdf-schema#label |
pemphigus vulgaris
|
gptkbp:ICD-10_code |
L10.0
|
gptkbp:MeSH_ID |
D010392
|
gptkbp:mortalityRate |
potentially fatal if untreated
|
gptkbp:namedFor |
gptkb:Willan
|
gptkbp:OMIM |
169610
|
gptkbp:onset |
middle-aged adults
|
gptkbp:prevalence |
rare
|
gptkbp:riskFactor |
genetic predisposition
certain HLA types |
gptkbp:symptom |
blisters
painful sores oral ulcers erosions |
gptkbp:treatment |
gptkb:rituximab
corticosteroids immunosuppressants |
gptkbp:bfsParent |
gptkb:rituximab
gptkb:Chris_Stein |
gptkbp:bfsLayer |
6
|