|
gptkbp:instanceOf
|
gptkb:autoimmune_disease
gptkb:skin
|
|
gptkbp:affects
|
gptkb:skin
mucous membranes
|
|
gptkbp:antibodyTarget
|
gptkb:desmoglein_1
gptkb:desmoglein_3
|
|
gptkbp:causedBy
|
autoantibodies
|
|
gptkbp:complication
|
infection
dehydration
|
|
gptkbp:diagnosedBy
|
gptkb:ELISA
biopsy
direct immunofluorescence
|
|
gptkbp:differentialDiagnosis
|
gptkb:bullous_pemphigoid
gptkb:mucous_membrane_pemphigoid
gptkb:lichen_planus
|
|
gptkbp:field
|
immunology
dermatology
|
|
gptkbp:firstDescribed
|
1788
|
|
gptkbp:ICD-10_code
|
L10.0
|
|
gptkbp:MeSH_ID
|
D010392
|
|
gptkbp:mortalityRate
|
potentially fatal if untreated
|
|
gptkbp:namedFor
|
gptkb:Willan
|
|
gptkbp:OMIM
|
169610
|
|
gptkbp:onset
|
middle-aged adults
|
|
gptkbp:prevalence
|
rare
|
|
gptkbp:riskFactor
|
genetic predisposition
certain HLA types
|
|
gptkbp:symptom
|
blisters
painful sores
oral ulcers
erosions
|
|
gptkbp:treatment
|
gptkb:rituximab
corticosteroids
immunosuppressants
|
|
gptkbp:bfsParent
|
gptkb:rituximab
gptkb:Chris_Stein
|
|
gptkbp:bfsLayer
|
6
|
|
https://www.w3.org/2000/01/rdf-schema#label
|
pemphigus vulgaris
|