pLGG

GPTKB entity

Statements (33)
Predicate Object
gptkbp:instanceOf brain tumor
gptkbp:affects children
gptkbp:age pediatric
gptkbp:associatedSyndrome gptkb:neurofibromatosis_type_1
gptkbp:commonSubtype gptkb:diffuse_astrocytoma
gptkb:pilocytic_astrocytoma
ganglioglioma
pleomorphic xanthoastrocytoma
gptkbp:diagnosedBy MRI
biopsy
gptkbp:fullName pediatric low-grade glioma
gptkbp:grades low-grade
gptkbp:growthForm slow-growing
https://www.w3.org/2000/01/rdf-schema#label pLGG
gptkbp:incidence most common pediatric brain tumor
gptkbp:location gptkb:spinal_cord
brain
gptkbp:mutationAssociatedWith gptkb:BRAF_V600E
NF1 mutation
BRAF-KIAA1549 fusion
gptkbp:prognosis generally favorable
gptkbp:recurrence possible
gptkbp:symptom nausea
vision problems
seizures
headaches
gptkbp:treatment surgery
radiation therapy
chemotherapy
gptkbp:WHOGrade II
I
gptkbp:bfsParent gptkb:LGG
gptkbp:bfsLayer 7