opsoclonus-myoclonus syndrome
GPTKB entity
Statements (29)
Predicate | Object |
---|---|
gptkbp:instanceOf |
neurological disorder
|
gptkbp:affects |
adults
children |
gptkbp:alsoKnownAs |
gptkb:OMS
gptkb:dancing_eyes-dancing_feet_syndrome |
gptkbp:associatedWith |
gptkb:neuroblastoma
viral infections paraneoplastic syndrome |
gptkbp:characterizedBy |
gptkb:opsoclonus
ataxia myoclonus behavioral disturbances |
gptkbp:firstDescribed |
1962
|
https://www.w3.org/2000/01/rdf-schema#label |
opsoclonus-myoclonus syndrome
|
gptkbp:ICD-10_code |
G25.8
|
gptkbp:MeSH_ID |
D009888
|
gptkbp:prognosis |
variable
|
gptkbp:symptom |
sleep disturbances
irritability unsteady gait muscle jerks rapid, involuntary eye movements |
gptkbp:treatment |
gptkb:rituximab
gptkb:ACTH immunotherapy corticosteroids intravenous immunoglobulin |
gptkbp:bfsParent |
gptkb:neuroblastoma
|
gptkbp:bfsLayer |
6
|