extraskeletal myxoid chondrosarcoma
GPTKB entity
Statements (38)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
rare soft tissue sarcoma
|
| gptkbp:age |
adults
|
| gptkbp:firstDescribed |
1953
Enzinger and Shiraki |
| gptkbp:has5YearSurvivalRate |
60-70%
|
| gptkbp:hasGeneticAlteration |
EWSR1-NR4A3 fusion
NR4A3 gene rearrangement |
| gptkbp:hasImagingFinding |
myxoid signal on MRI
well-circumscribed mass |
| gptkbp:hasImmunohistochemistryMarker |
gptkb:vimentin
S100 protein (variable) |
| gptkbp:hasLocation |
soft tissues
|
| gptkbp:hasMetastasisSite |
gptkb:cancer
gptkb:bone lymph nodes |
| gptkbp:hasPeakIncidenceAge |
40-60 years
|
| gptkbp:hasSexRatio |
male predominance
|
| gptkbp:histology |
cords and strands of tumor cells
myxoid matrix |
| https://www.w3.org/2000/01/rdf-schema#label |
extraskeletal myxoid chondrosarcoma
|
| gptkbp:ICD-10_code |
C49.A
|
| gptkbp:location |
trunk
limbs proximal extremities |
| gptkbp:originatedIn |
mesenchymal cells
|
| gptkbp:prevalence |
less than 3% of all soft tissue sarcomas
|
| gptkbp:prognosis |
indolent course
risk of local recurrence risk of metastasis |
| gptkbp:recurrence |
high
|
| gptkbp:synonym |
gptkb:EMC
extraskeletal myxoid chondrosarcoma tumor |
| gptkbp:treatment |
radiation therapy
chemotherapy surgical excision |
| gptkbp:WHOClassification |
malignant soft tissue tumor
|
| gptkbp:bfsParent |
gptkb:NR4A3
|
| gptkbp:bfsLayer |
7
|