dystrophin-related protein

GPTKB entity

Statements (23)
Predicate Object
gptkbp:instanceOf gptkb:protein
gptkbp:alsoKnownAs gptkb:utrophin
gptkbp:discoveredIn 1989
gptkbp:domain C-terminal domain
actin-binding domain
spectrin-like repeats
gptkbp:encodedBy gptkb:UTRN_gene
gptkbp:foundIn humans
other vertebrates
gptkbp:function cytoskeletal protein
links cytoskeleton to extracellular matrix
https://www.w3.org/2000/01/rdf-schema#label dystrophin-related protein
gptkbp:involves Duchenne muscular dystrophy (compensatory role)
gptkbp:location gptkb:skeletal_muscle
neuromuscular junction
gptkbp:molecularWeight 395 kDa
gptkbp:orthologIn gptkb:dystrophin
gptkbp:relatedTo gptkb:dystrophin
gptkbp:role muscle development
muscle regeneration
gptkbp:structure rod-shaped
gptkbp:bfsParent gptkb:utrophin
gptkbp:bfsLayer 7