carnitine palmitoyltransferase 1

GPTKB entity

Statements (26)
Predicate Object
gptkbp:instanceOf gptkb:enzyme
gptkbp:associatedWith carnitine palmitoyltransferase I deficiency
gptkbp:EC_number 2.3.1.21
gptkbp:foundIn gptkb:skeletal_muscle
brain
liver
gptkbp:function catalyzes the transfer of long-chain fatty acids into mitochondria
gptkbp:gene gptkb:CPT1A
CPT1B
CPT1C
https://www.w3.org/2000/01/rdf-schema#label carnitine palmitoyltransferase 1
gptkbp:inhibitedBy gptkb:malonyl-CoA
gptkbp:involvedIn fatty acid beta-oxidation
gptkbp:location outer mitochondrial membrane
gptkbp:otherName CPT I
CPT1
gptkbp:product gptkb:CoA
palmitoylcarnitine
gptkbp:substrate gptkb:carnitine
palmitoyl-CoA
gptkbp:systematicName palmitoyl-CoA:L-carnitine O-palmitoyltransferase
gptkbp:UniProtID P50416 (CPT1A)
Q7Z2E3 (CPT1B)
Q8TCG1 (CPT1C)
gptkbp:bfsParent gptkb:malonyl-CoA
gptkbp:bfsLayer 7