carnitine

GPTKB entity

Statements (57)
Predicate Object
gptkbp:instanceOf nutritionist
quaternary ammonium compound
gptkbp:absorption gptkb:small_intestine
gptkbp:approvedBy gptkb:European_Union
gptkb:Japan
gptkb:United_States
gptkbp:ATCCode A16AA01
gptkbp:biosynthesized_from lysine
methionine
gptkbp:CASNumber 541-15-1
gptkbp:category dietary supplement
nutraceutical
metabolite
zwitterion
amino acid derivative
organic cation transporter substrate
gptkbp:chemicalFormula C7H15NO3
gptkbp:deficiencyCauses gptkb:hypoglycemia
muscle weakness
cardiomyopathy
fatty liver
gptkbp:discoveredBy gptkb:Vladimir_Gulevich
gptkbp:discoveredIn 1905
gptkbp:excretion urine
gptkbp:foundIn gptkb:meat
dairy products
animal tissues
gptkbp:function energy production
transport of fatty acids into mitochondria
https://www.w3.org/2000/01/rdf-schema#label carnitine
gptkbp:IUPACName (R)-3-hydroxy-4-(trimethylazaniumyl)butanoate
gptkbp:medicalUse gptkb:secondary_carnitine_deficiency
gptkb:valproic_acid_toxicity
gptkb:primary_carnitine_deficiency
gptkbp:meltingPoint 197 °C
gptkbp:molecularWeight 161.2 g/mol
gptkbp:regulates regulated by kidneys
gptkbp:relatedTo gptkb:acetylcarnitine
gptkb:propionylcarnitine
gptkbp:requires fatty acid oxidation
gptkbp:routeOfAdministration oral
intramuscular
intravenous
gptkbp:sideEffect nausea
vomiting
diarrhea
fishy body odor
gptkbp:solubility very soluble
gptkbp:storage gptkb:skeletal_muscle
gptkb:kidney
heart
liver
gptkbp:bfsParent gptkb:Q9UM73
gptkb:Magnetic_Resonance_Spectroscopy
gptkb:OCTN2_protein
gptkb:solute_carrier_family_22_member_5
gptkbp:bfsLayer 7