Statements (37)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:disease
gptkb:histiocytic_disorder rare disease |
| gptkbp:affects |
gptkb:Titan
gptkb:skin children young adults central nervous system nasal cavity extranodal sites |
| gptkbp:alsoKnownAs |
sinus histiocytosis with massive lymphadenopathy
|
| gptkbp:commonIn |
cervical lymph nodes
|
| gptkbp:diagnosedBy |
lymph node biopsy
|
| gptkbp:etiology |
unknown
|
| gptkbp:firstDescribed |
1969
Juan Rosai Ronald Dorfman |
| gptkbp:histology |
S100 positive histiocytes
emperipolesis |
| https://www.w3.org/2000/01/rdf-schema#label |
Rosai-Dorfman disease
|
| gptkbp:ICD-10_code |
D76.3
|
| gptkbp:namedAfter |
Juan Rosai
Ronald Dorfman |
| gptkbp:OMIM |
268700
|
| gptkbp:possibleRelation |
gptkb:virus
immune dysfunction |
| gptkbp:prognosis |
generally good
|
| gptkbp:symptom |
fever
weight loss night sweats painless lymphadenopathy |
| gptkbp:treatment |
astronomer
radiation therapy chemotherapy corticosteroids |
| gptkbp:bfsParent |
gptkb:Langerhans_cell_histiocytosis
|
| gptkbp:bfsLayer |
6
|