Pemphigus

GPTKB entity

Statements (31)
Predicate Object
gptkbp:instanceOf gptkb:skin
autoimmune disease
gptkbp:affects gptkb:skin
mucous membranes
gptkbp:antibodyTarget desmoglein
gptkbp:canBeFatal yes
gptkbp:causedBy autoantibodies
gptkbp:characterizedBy blisters
erosions
gptkbp:diagnosedBy skin biopsy
direct immunofluorescence
gptkbp:firstDescribed gptkb:Willan
18th century
https://www.w3.org/2000/01/rdf-schema#label Pemphigus
gptkbp:ICD-10_code gptkb:L10
gptkbp:notableCase Flavius Josephus (possible historical case)
gptkbp:onset middle-aged adults
gptkbp:prevalence rare
gptkbp:riskFactor genetic predisposition
certain drugs
gptkbp:subspecies gptkb:Paraneoplastic_pemphigus
gptkb:Pemphigus_foliaceus
gptkb:Pemphigus_vegetans
gptkb:Pemphigus_vulgaris
gptkbp:symptom oral ulcers
painful blisters
skin erosions
gptkbp:treatment corticosteroids
immunosuppressants
gptkbp:bfsParent gptkb:Aphididae
gptkbp:bfsLayer 6