Medium-chain acyl-CoA dehydrogenase

GPTKB entity

Statements (23)
Predicate Object
gptkbp:instanceOf gptkb:enzyme
gptkbp:associatedWith sudden infant death syndrome
hypoketotic hypoglycemia
gptkbp:catalyzes oxidation of medium-chain fatty acids
gptkbp:cofactor gptkb:FAD
gptkbp:deficiencyCauses gptkb:medium-chain_acyl-CoA_dehydrogenase_deficiency
gptkbp:EC_number 1.3.8.7
gptkbp:encodedBy gptkb:ACADM_gene
gptkbp:foundIn mitochondria
gptkbp:gene gptkb:ACADM
https://www.w3.org/2000/01/rdf-schema#label Medium-chain acyl-CoA dehydrogenase
gptkbp:involves fatty acid beta-oxidation
gptkbp:locatedOnChromosome 1p31
gptkbp:molecularWeight ~45 kDa
gptkbp:OMIM 607008
gptkbp:product reduced electron transfer flavoprotein
trans-2,3-enoyl-CoA
gptkbp:species gptkb:Homo_sapiens
gptkbp:structure homotetramer
gptkbp:substrate medium-chain acyl-CoA esters
gptkbp:UniProtID P11310
gptkbp:bfsParent gptkb:MCAD
gptkbp:bfsLayer 5