Medium-chain acyl-CoA dehydrogenase
GPTKB entity
Statements (23)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:enzyme
|
| gptkbp:associatedWith |
sudden infant death syndrome
hypoketotic hypoglycemia |
| gptkbp:catalyzes |
oxidation of medium-chain fatty acids
|
| gptkbp:cofactor |
gptkb:FAD
|
| gptkbp:deficiencyCauses |
gptkb:medium-chain_acyl-CoA_dehydrogenase_deficiency
|
| gptkbp:EC_number |
1.3.8.7
|
| gptkbp:encodedBy |
gptkb:ACADM_gene
|
| gptkbp:foundIn |
mitochondria
|
| gptkbp:gene |
gptkb:ACADM
|
| gptkbp:involves |
fatty acid beta-oxidation
|
| gptkbp:locatedOnChromosome |
1p31
|
| gptkbp:molecularWeight |
~45 kDa
|
| gptkbp:OMIM |
607008
|
| gptkbp:product |
reduced electron transfer flavoprotein
trans-2,3-enoyl-CoA |
| gptkbp:species |
gptkb:Homo_sapiens
|
| gptkbp:structure |
homotetramer
|
| gptkbp:substrate |
medium-chain acyl-CoA esters
|
| gptkbp:UniProtID |
P11310
|
| gptkbp:bfsParent |
gptkb:MCAD
|
| gptkbp:bfsLayer |
5
|
| https://www.w3.org/2000/01/rdf-schema#label |
Medium-chain acyl-CoA dehydrogenase
|