Medium-chain acyl-CoA dehydrogenase
GPTKB entity
Statements (23)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:enzyme
|
gptkbp:associatedWith |
sudden infant death syndrome
hypoketotic hypoglycemia |
gptkbp:catalyzes |
oxidation of medium-chain fatty acids
|
gptkbp:cofactor |
gptkb:FAD
|
gptkbp:deficiencyCauses |
gptkb:medium-chain_acyl-CoA_dehydrogenase_deficiency
|
gptkbp:EC_number |
1.3.8.7
|
gptkbp:encodedBy |
gptkb:ACADM_gene
|
gptkbp:foundIn |
mitochondria
|
gptkbp:gene |
gptkb:ACADM
|
https://www.w3.org/2000/01/rdf-schema#label |
Medium-chain acyl-CoA dehydrogenase
|
gptkbp:involves |
fatty acid beta-oxidation
|
gptkbp:locatedOnChromosome |
1p31
|
gptkbp:molecularWeight |
~45 kDa
|
gptkbp:OMIM |
607008
|
gptkbp:product |
reduced electron transfer flavoprotein
trans-2,3-enoyl-CoA |
gptkbp:species |
gptkb:Homo_sapiens
|
gptkbp:structure |
homotetramer
|
gptkbp:substrate |
medium-chain acyl-CoA esters
|
gptkbp:UniProtID |
P11310
|
gptkbp:bfsParent |
gptkb:MCAD
|
gptkbp:bfsLayer |
5
|