Epithelioid Hemangioendothelioma

URI: https://gptkb.org/entity/Epithelioid_Hemangioendothelioma
GPTKB entity
Statements (37)
Predicate Object
gptkbp:instanceOf rare cancer
vascular tumor
gptkbp:affects gptkb:cancer
gptkb:bone
liver
soft tissue
gptkbp:canMetastasizeTo yes
gptkbp:firstDescribed 1982
gptkbp:hasGenderPredilection slight female predominance
gptkbp:hasGeneticAlteration gptkb:WWTR1-CAMTA1_fusion
gptkb:YAP1-TFE3_fusion
gptkbp:hasImmunohistochemistryMarker gptkb:CD34
gptkb:CD31
gptkb:Factor_VIII-related_antigen
gptkbp:hasMalignancy intermediate
gptkbp:histology epithelioid endothelial cells
https://www.w3.org/2000/01/rdf-schema#label Epithelioid Hemangioendothelioma
gptkbp:ICD-10_code C49.A
gptkbp:medianAge 30-50 years
gptkbp:originatedIn endothelial cells
gptkbp:prevalence very rare
gptkbp:prognosis variable
gptkbp:referencedIn gptkb:MeSH:D018223
gptkb:OMIM:607709
gptkb:Orphanet:_ORPHA:2840
gptkbp:riskFactor unknown
gptkbp:symptom pain
fatigue
weight loss
swelling
gptkbp:synonym gptkb:EHE
gptkbp:treatment surgery
radiation therapy
chemotherapy
targeted therapy
gptkbp:bfsParent gptkb:EHE
gptkbp:bfsLayer 6