Statements (13)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:protein
|
gptkbp:alternativeName |
PDH E1-alpha
|
gptkbp:associatedWith |
gptkb:pyruvate_dehydrogenase_deficiency
|
gptkbp:cofactor |
thiamine pyrophosphate
|
gptkbp:component |
gptkb:pyruvate_dehydrogenase_complex
|
gptkbp:encodedBy |
PDHA1 gene
|
gptkbp:formsComplexWith |
E1-beta subunit
|
gptkbp:function |
catalyzes decarboxylation of pyruvate
|
https://www.w3.org/2000/01/rdf-schema#label |
E1-alpha subunit
|
gptkbp:location |
mitochondrial matrix
|
gptkbp:molecularWeight |
~43 kDa
|
gptkbp:bfsParent |
gptkb:branched-chain_alpha-keto_acid_dehydrogenase_E1_alpha_subunit
|
gptkbp:bfsLayer |
8
|