|
gptkbp:instanceOf
|
gptkb:disease
gptkb:vasculitis
|
|
gptkbp:abbreviation
|
gptkb:EGPA
|
|
gptkbp:affects
|
medium blood vessels
small blood vessels
|
|
gptkbp:alsoKnownAs
|
gptkb:eosinophilic_granulomatosis_with_polyangiitis
|
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gptkbp:associatedWith
|
gptkb:antineutrophil_cytoplasmic_antibodies
|
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gptkbp:category
|
gptkb:autoimmune_disease
gptkb:systemic_vasculitis
gptkb:rare_disease
|
|
gptkbp:cause
|
autoimmune
|
|
gptkbp:characterizedBy
|
gptkb:vasculitis
asthma
granulomatous inflammation
eosinophilia
|
|
gptkbp:complication
|
gptkb:peripheral_neuropathy
heart failure
renal failure
|
|
gptkbp:diagnosedBy
|
gptkb:blood_test
imaging
clinical criteria
biopsy
|
|
gptkbp:firstDescribed
|
gptkb:Jacob_Churg
gptkb:Lotte_Strauss
1951
|
|
gptkbp:ICD-10_code
|
M30.1
|
|
gptkbp:prevalence
|
rare
|
|
gptkbp:symptom
|
gptkb:sinusitis
gptkb:peripheral_neuropathy
asthma
fever
abdominal pain
joint pain
muscle pain
weight loss
skin rash
cardiac involvement
|
|
gptkbp:treatment
|
biologics
corticosteroids
immunosuppressive drugs
|
|
gptkbp:bfsParent
|
gptkb:Lotte_Strauss
|
|
gptkbp:bfsLayer
|
8
|
|
https://www.w3.org/2000/01/rdf-schema#label
|
Churg–Strauss syndrome
|