Antley-Bixler syndrome

GPTKB entity

Statements (28)
Predicate Object
gptkbp:instanceOf gptkb:genetic_disorder
gptkb:rare_disease
gptkbp:affects skeletal system
craniofacial development
gptkbp:causedBy mutation in FGFR2 gene
mutation in POR gene
gptkbp:firstDescribed 1975
gptkbp:ICD-10_code Q87.0
gptkbp:inheritance autosomal dominant
autosomal recessive
gptkbp:namedAfter gptkb:David_Bixler
Robert M. Antley
gptkbp:OMIM 207410
gptkbp:prevalence very rare
gptkbp:symptom genital anomalies
midface hypoplasia
joint contractures
craniosynostosis
choanal atresia
bowed femora
radiohumeral synostosis
gptkbp:synonym craniosynostosis with radiohumeral synostosis
gptkbp:treatment supportive care
surgical intervention
gptkbp:bfsParent gptkb:FGFR2_gene
gptkb:FGFR2
gptkbp:bfsLayer 8
https://www.w3.org/2000/01/rdf-schema#label Antley-Bixler syndrome

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