Statements (49)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:cancer
gptkb:disease gptkb:rhabdomyosarcoma |
| gptkbp:affects |
gptkb:breast
gptkb:skin heart liver blood vessels lymphatic vessels deep soft tissue |
| gptkbp:firstDescribed |
gptkb:Malassez
1879 |
| gptkbp:frequency |
less than 2% of all sarcomas
|
| gptkbp:hasEpidemiology |
rare
|
| gptkbp:hasNotableSubtype |
cardiac angiosarcoma
hepatic angiosarcoma breast angiosarcoma cutaneous angiosarcoma lymphangiosarcoma |
| gptkbp:hasOrphanetID |
ORPHA:318
|
| gptkbp:hasTypicalOnset |
elderly
adulthood |
| gptkbp:histology |
malignant endothelial cells
|
| https://www.w3.org/2000/01/rdf-schema#label |
Angiosarcoma
|
| gptkbp:ICD-10_code |
C38.0
C46.0 C49.9 |
| gptkbp:MeSH_ID |
D018223
|
| gptkbp:mortalityRate |
high
|
| gptkbp:prognosis |
poor
|
| gptkbp:riskFactor |
radiation exposure
chemical exposure arsenic exposure thorium dioxide exposure vinyl chloride exposure chronic lymphedema foreign body implants |
| gptkbp:subclassOf |
gptkb:rhabdomyosarcoma
vascular tumor |
| gptkbp:symptom |
pain
ulceration swelling skin lesion |
| gptkbp:synonym |
malignant hemangioendothelioma
|
| gptkbp:treatment |
surgery
radiation therapy chemotherapy |
| gptkbp:bfsParent |
gptkb:rhabdomyosarcoma
|
| gptkbp:bfsLayer |
5
|