|
gptkbp:instanceOf
|
gptkb:autoimmune_disease
gptkb:inflammatory_myopathy
|
|
gptkbp:affects
|
gptkb:skin
children
muscles
|
|
gptkbp:autoantibody
|
gptkb:anti-p155/140
gptkb:anti-MDA5
gptkb:anti-Mi-2
gptkb:anti-NXP2
|
|
gptkbp:cause
|
gptkb:unknown
|
|
gptkbp:complication
|
gptkb:lipodystrophy
contractures
calcinosis
vasculopathy
|
|
gptkbp:diagnosedBy
|
gptkb:EMG
MRI
muscle biopsy
blood tests
|
|
gptkbp:firstDescribed
|
1891
|
|
gptkbp:gender
|
more common in females
|
|
gptkbp:ICD-10_code
|
gptkb:M33.0
|
|
gptkbp:parent
|
gptkb:dermatomyositis
idiopathic inflammatory myopathy
|
|
gptkbp:prevalence
|
rare
2-4 per million children per year
|
|
gptkbp:prognosis
|
variable
improved with early treatment
|
|
gptkbp:riskFactor
|
genetic predisposition
environmental triggers
|
|
gptkbp:signature
|
gptkb:Gottron's_papules
gptkb:V-sign
gptkb:shawl_sign
heliotrope rash
nailfold capillary changes
periorbital edema
proximal muscle weakness
|
|
gptkbp:symptom
|
fatigue
joint pain
muscle weakness
skin rash
dysphagia
calcinosis
|
|
gptkbp:treatment
|
gptkb:methotrexate
gptkb:IVIG
physical therapy
corticosteroids
immunosuppressive drugs
|
|
gptkbp:bfsParent
|
gptkb:dermatomyositis
|
|
gptkbp:bfsLayer
|
8
|
|
https://www.w3.org/2000/01/rdf-schema#label
|
juvenile dermatomyositis
|