glutaryl-CoA dehydrogenase (enzyme)

GPTKB entity

Statements (19)
Predicate Object
gptkbp:instanceOf gptkb:enzyme
gptkbp:catalyzes oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA
gptkbp:cofactor gptkb:FAD
gptkbp:deficiencyCauses gptkb:glutaric_aciduria_type_I
gptkbp:EC_number 1.3.8.6
gptkbp:encodedBy GCDH gene
gptkbp:foundIn mitochondria
https://www.w3.org/2000/01/rdf-schema#label glutaryl-CoA dehydrogenase (enzyme)
gptkbp:involves lysine degradation
hydroxylysine degradation
tryptophan degradation
gptkbp:presentIn humans
other mammals
gptkbp:product CO2
reduced electron transfer flavoprotein
crotonyl-CoA
gptkbp:substrate glutaryl-CoA
gptkbp:bfsParent gptkb:GCDH
gptkbp:bfsLayer 7