glutaryl-CoA dehydrogenase (enzyme)
GPTKB entity
Statements (19)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:enzyme
|
gptkbp:catalyzes |
oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA
|
gptkbp:cofactor |
gptkb:FAD
|
gptkbp:deficiencyCauses |
gptkb:glutaric_aciduria_type_I
|
gptkbp:EC_number |
1.3.8.6
|
gptkbp:encodedBy |
GCDH gene
|
gptkbp:foundIn |
mitochondria
|
https://www.w3.org/2000/01/rdf-schema#label |
glutaryl-CoA dehydrogenase (enzyme)
|
gptkbp:involves |
lysine degradation
hydroxylysine degradation tryptophan degradation |
gptkbp:presentIn |
humans
other mammals |
gptkbp:product |
CO2
reduced electron transfer flavoprotein crotonyl-CoA |
gptkbp:substrate |
glutaryl-CoA
|
gptkbp:bfsParent |
gptkb:GCDH
|
gptkbp:bfsLayer |
7
|