clear cell sarcoma

GPTKB entity

Statements (33)
Predicate Object
gptkbp:instanceOf gptkb:cancer
gptkb:rhabdomyosarcoma
gptkbp:affects tendons
soft tissue
aponeuroses
gptkbp:age adolescents
young adults
gptkbp:alsoKnownAs malignant melanoma of soft parts
gptkbp:canMetastasizeTo gptkb:cancer
lymph nodes
gptkbp:firstDescribed 1965
Enzinger
gptkbp:hasGeneticAlteration EWSR1-ATF1 fusion
gptkbp:histology clear cytoplasm
nested growth pattern
https://www.w3.org/2000/01/rdf-schema#label clear cell sarcoma
gptkbp:ICD-10_code gptkb:C49
gptkbp:location knee
foot
ankle
lower extremities
gptkbp:marking HMB-45 positive
Melan-A positive
S100 positive
gptkbp:MeSH_ID D018223
gptkbp:OMIM 606219
gptkbp:prognosis poor
gptkbp:treatment radiation therapy
chemotherapy
surgical excision
gptkbp:bfsParent gptkb:ATF1
gptkb:EWSR1
gptkbp:bfsLayer 7