Statements (37)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:disease
leukemia |
| gptkbp:affects |
gptkb:skin
blood lymph nodes |
| gptkbp:affectsDemographic |
older adults
|
| gptkbp:associatedWith |
chromosome 17q11-q12
|
| gptkbp:causedBy |
malignant proliferation of T-cells
|
| gptkbp:differentialDiagnosis |
gptkb:eczema
gptkb:atopic_dermatitis psoriasis |
| gptkbp:firstDescribed |
1938
|
| gptkbp:hasDiagnosticMethod |
blood smear
skin biopsy flow cytometry |
| gptkbp:hasType |
CD4+ T-cells
Sézary cells |
| https://www.w3.org/2000/01/rdf-schema#label |
Sézary syndrome
|
| gptkbp:ICD-10_code |
C84.1
|
| gptkbp:MeSH_ID |
D012704
|
| gptkbp:mortalityRate |
high
|
| gptkbp:namedAfter |
Albert Sézary
|
| gptkbp:OMIM |
254400
|
| gptkbp:prevalence |
rare
|
| gptkbp:prognosis |
poor
|
| gptkbp:subspecies |
gptkb:mycosis_fungoides
|
| gptkbp:symptom |
pruritus
lymphadenopathy erythroderma presence of Sézary cells in blood |
| gptkbp:treatment |
chemotherapy
immunotherapy stem cell transplant retinoids photopheresis |
| gptkbp:bfsParent |
gptkb:leukemia
|
| gptkbp:bfsLayer |
5
|