Multicentric angioimmunoblastic lymphadenopathy with dysproteinemia
GPTKB entity
Statements (25)
Predicate | Object |
---|---|
gptkbp:instanceOf |
gptkb:disease
lymphoproliferative disorder |
gptkbp:affects |
immune system
lymphatic system |
gptkbp:alsoKnownAs |
gptkb:angioimmunoblastic_T-cell_lymphoma
|
gptkbp:causedBy |
unknown
|
gptkbp:firstDescribed |
1970s
|
gptkbp:hasFinding |
abnormal lymph node architecture
autoimmune phenomena dysproteinemia immune dysfunction polyclonal hypergammaglobulinemia |
https://www.w3.org/2000/01/rdf-schema#label |
Multicentric angioimmunoblastic lymphadenopathy with dysproteinemia
|
gptkbp:prognosis |
poor
|
gptkbp:symptom |
gptkb:anemia
fever weight loss hepatosplenomegaly lymphadenopathy skin rash |
gptkbp:treatment |
chemotherapy
immunosuppressive therapy corticosteroids |
gptkbp:bfsParent |
gptkb:MALS
|
gptkbp:bfsLayer |
6
|