Multicentric angioimmunoblastic lymphadenopathy with dysproteinemia
GPTKB entity
Statements (25)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:lymphoproliferative_disorder
gptkb:disease |
| gptkbp:affects |
immune system
lymphatic system |
| gptkbp:alsoKnownAs |
gptkb:angioimmunoblastic_T-cell_lymphoma
|
| gptkbp:causedBy |
gptkb:unknown
|
| gptkbp:firstDescribed |
1970s
|
| gptkbp:hasFinding |
abnormal lymph node architecture
autoimmune phenomena dysproteinemia immune dysfunction polyclonal hypergammaglobulinemia |
| gptkbp:prognosis |
poor
|
| gptkbp:symptom |
gptkb:anemia
fever weight loss hepatosplenomegaly lymphadenopathy skin rash |
| gptkbp:treatment |
chemotherapy
immunosuppressive therapy corticosteroids |
| gptkbp:bfsParent |
gptkb:MALS
|
| gptkbp:bfsLayer |
6
|
| https://www.w3.org/2000/01/rdf-schema#label |
Multicentric angioimmunoblastic lymphadenopathy with dysproteinemia
|