Multicentric angioimmunoblastic lymphadenopathy with dysproteinemia

GPTKB entity

Statements (25)
Predicate Object
gptkbp:instanceOf gptkb:disease
lymphoproliferative disorder
gptkbp:affects immune system
lymphatic system
gptkbp:alsoKnownAs gptkb:angioimmunoblastic_T-cell_lymphoma
gptkbp:causedBy unknown
gptkbp:firstDescribed 1970s
gptkbp:hasFinding abnormal lymph node architecture
autoimmune phenomena
dysproteinemia
immune dysfunction
polyclonal hypergammaglobulinemia
https://www.w3.org/2000/01/rdf-schema#label Multicentric angioimmunoblastic lymphadenopathy with dysproteinemia
gptkbp:prognosis poor
gptkbp:symptom gptkb:anemia
fever
weight loss
hepatosplenomegaly
lymphadenopathy
skin rash
gptkbp:treatment chemotherapy
immunosuppressive therapy
corticosteroids
gptkbp:bfsParent gptkb:MALS
gptkbp:bfsLayer 6