Mitochondrial trifunctional protein
GPTKB entity
Statements (23)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:protein
|
| gptkbp:associatedWith |
gptkb:Mitochondrial_trifunctional_protein_deficiency
|
| gptkbp:catalyzes |
long-chain 3-hydroxyacyl-CoA dehydrogenase activity
long-chain 3-ketoacyl-CoA thiolase activity long-chain enoyl-CoA hydratase activity |
| gptkbp:discoveredBy |
1992
|
| gptkbp:EC_number |
1.1.1.211
2.3.1.16 4.2.1.17 |
| gptkbp:foundIn |
eukaryotes
|
| gptkbp:function |
fatty acid beta-oxidation
|
| gptkbp:gene |
gptkb:HADHA
gptkb:HADHB |
| https://www.w3.org/2000/01/rdf-schema#label |
Mitochondrial trifunctional protein
|
| gptkbp:location |
mitochondrial inner membrane
|
| gptkbp:molecularWeight |
~400 kDa
|
| gptkbp:OMIM |
609015
|
| gptkbp:structure |
heterooctamer (4 alpha and 4 beta subunits)
|
| gptkbp:subunit |
gptkb:HADHA
gptkb:HADHB |
| gptkbp:UniProtID |
gptkb:Q9UIJ7
|
| gptkbp:bfsParent |
gptkb:MTP
|
| gptkbp:bfsLayer |
6
|