Loeys-Dietz syndrome type 3

GPTKB entity

Statements (23)
Predicate Object
gptkbp:instanceOf gptkb:syndrome
gptkb:genetic_disorder
gptkbp:causedBy SMAD3 gene mutation
gptkbp:complication early-onset osteoarthritis
arterial dissection
gptkbp:containsGene gptkb:SMAD3
gptkbp:frequency rare
gptkbp:inheritance autosomal dominant
gptkbp:OMIM 613795
gptkbp:onset childhood
gptkbp:subspecies gptkb:Loeys-Dietz_syndrome
gptkbp:symptom aortic aneurysm
skeletal abnormalities
hypertelorism
cleft palate
joint hypermobility
arterial tortuosity
gptkbp:treatment gptkb:angiotensin_receptor_blockers
beta-blockers
surgical repair of aneurysms
gptkbp:bfsParent gptkb:Loeys-Dietz_syndrome
gptkbp:bfsLayer 8
https://www.w3.org/2000/01/rdf-schema#label Loeys-Dietz syndrome type 3