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Extramammary Paget's disease
URI:
https://gptkb.org/entity/Extramammary_Paget's_disease
GPTKB entity
Statements (43)
Predicate
Object
gptkbp:instanceOf
gptkb:disease
gptkb:skin
rare disease
gptkbp:affects
gptkb:skin
apocrine gland-bearing areas
gptkbp:associatedWith
underlying malignancy
gptkbp:canMetastasizeTo
yes
gptkbp:diagnosedBy
skin biopsy
gptkbp:differentialDiagnosis
gptkb:eczema
gptkb:Bowen's_disease
gptkb:lichen_sclerosus
psoriasis
gptkbp:firstDescribed
1889
gptkbp:histology
gptkb:Paget_cells
https://www.w3.org/2000/01/rdf-schema#label
Extramammary Paget's disease
gptkbp:ICD-10_code
C51.0
C60.0
C63.2
gptkbp:location
gptkb:scrotum
gptkb:axilla
penis
vulva
perianal region
gptkbp:MeSH_ID
D010267
gptkbp:namedAfter
gptkb:Sir_James_Paget
gptkbp:prognosis
variable
gptkbp:recurrence
high
gptkbp:relatedTo
gptkb:mammary_Paget's_disease
gptkbp:riskFactor
older age
female sex
gptkbp:subspecies
primary extramammary Paget's disease
secondary extramammary Paget's disease
gptkbp:symptom
pain
scaling
itching
redness
ulceration
gptkbp:treatment
gptkb:Mohs_micrographic_surgery
radiation therapy
surgical excision
topical chemotherapy
gptkbp:bfsParent
gptkb:Paget's_disease
gptkbp:bfsLayer
6