DiGeorge syndrome

GPTKB entity

Statements (37)
Predicate Object
gptkbp:instanceOf gptkb:genetic_disorder
gptkbp:affects gptkb:thymus
heart
parathyroid glands
palate
gptkbp:alsoKnownAs gptkb:22q11.2_deletion_syndrome
gptkb:velocardiofacial_syndrome
gptkbp:causedBy deletion on chromosome 22q11.2
gptkbp:diagnosedBy genetic testing
gptkbp:firstDescribed gptkb:Angelo_DiGeorge
1968
gptkbp:ICD-10_code D82.1
gptkbp:inheritance autosomal dominant
gptkbp:OMIM 188400
gptkbp:prevalence 1 in 4,000 live births
gptkbp:riskFactor gptkb:autoimmune_disease
gptkb:autism_spectrum_disorder
schizophrenia
seizures
gptkbp:symptom congenital heart defects
developmental delay
learning difficulties
cleft palate
immune deficiency
psychiatric disorders
hypocalcemia
gptkbp:treatment cardiac surgery
symptomatic management
calcium supplementation
immune system support
gptkbp:bfsParent gptkb:Thymus
gptkb:neural_crest_cells
gptkb:Tetralogy_of_Fallot
gptkb:thymus
gptkb:tetralogy_of_Fallot
gptkbp:bfsLayer 7
https://www.w3.org/2000/01/rdf-schema#label DiGeorge syndrome

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