Chronic Histiocytic Syndrome
GPTKB entity
Statements (32)
| Predicate | Object |
|---|---|
| gptkbp:instanceOf |
gptkb:disease
|
| gptkbp:affects |
gptkb:skin
lungs liver lymph nodes bones bone marrow immune system |
| gptkbp:alsoKnownAs |
gptkb:Histiocytosis_X
gptkb:Langerhans_cell_histiocytosis |
| gptkbp:characterizedBy |
abnormal proliferation of histiocytes
|
| gptkbp:diagnosedBy |
biopsy
blood tests imaging studies |
| gptkbp:firstDescribed |
1939
|
| https://www.w3.org/2000/01/rdf-schema#label |
Chronic Histiocytic Syndrome
|
| gptkbp:ICD-10_code |
C96.6
|
| gptkbp:rareDisease |
true
|
| gptkbp:relatedTo |
Hand-Schüller-Christian disease
Letterer-Siwe disease |
| gptkbp:symptom |
fever
enlarged liver enlarged spleen weight loss bone pain skin rash |
| gptkbp:treatment |
surgery
radiation therapy chemotherapy corticosteroids |
| gptkbp:bfsParent |
gptkb:CHS
|
| gptkbp:bfsLayer |
7
|