Adenoid Cystic Carcinoma

GPTKB entity

Statements (50)
Predicate Object
gptkbp:instanceOf gptkb:cancer
Malignant tumor
gptkbp:affects gptkb:Lacrimal_gland
gptkb:Trachea
gptkb:Vulva
gptkb:skin
Both sexes
Breast
Salivary glands
Sinuses
Major salivary glands
Minor salivary glands
gptkbp:affectsAgeGroup Middle-aged adults
gptkbp:characteristic Perineural invasion
High recurrence rate
Slow-growing
Tendency for late metastasis
gptkbp:firstDescribed gptkb:Theodor_Billroth
1859
gptkbp:hasGeneticAlteration gptkb:MYB-NFIB_fusion
gptkb:MYBL1-NFIB_fusion
gptkbp:hasMetastasisSite gptkb:bone
Liver
Lung
gptkbp:histology Cribriform pattern
Solid pattern
Tubular pattern
https://www.w3.org/2000/01/rdf-schema#label Adenoid Cystic Carcinoma
gptkbp:ICD-10_code gptkb:C07
C08
gptkbp:incidence 10% of all salivary gland tumors
Less than 1% of all head and neck cancers
gptkbp:prevalence Rare
gptkbp:prognosis Variable
Poor long-term survival
gptkbp:symptom gptkb:Pain
Difficulty swallowing
Facial nerve paralysis
Painless mass
Ulceration
gptkbp:synonym gptkb:ACC
gptkbp:treatment radiation therapy
Chemotherapy
Surgical excision
gptkbp:website gptkb:Palate
gptkb:Parotid_gland
gptkb:Submandibular_gland
gptkbp:bfsParent gptkb:ACC
gptkb:AAC
gptkbp:bfsLayer 6