round cell liposarcoma

GPTKB entity

Statements (22)
Predicate Object
gptkbp:instanceOf liposarcoma subtype
gptkbp:age adults
gptkbp:associated_gene_fusion FUS-DDIT3
gptkbp:associatedWith t(12;16)(q13;p11) translocation
gptkbp:common_site retroperitoneum
deep soft tissues of extremities
gptkbp:firstDescribed mid-20th century
gptkbp:has_malignant_potential high
gptkbp:histological_feature high nuclear-to-cytoplasmic ratio
scant cytoplasm
round primitive cells
https://www.w3.org/2000/01/rdf-schema#label round cell liposarcoma
gptkbp:prognosis worse than myxoid liposarcoma
gptkbp:subclassOf gptkb:myxoid_liposarcoma
gptkbp:treatment radiation therapy
chemotherapy
surgical excision
gptkbp:type gptkb:rhabdomyosarcoma
adipocytic tumor
malignant soft tissue tumor
gptkbp:bfsParent gptkb:myxoid_liposarcoma
gptkbp:bfsLayer 7