mandibuloacral dysplasia

GPTKB entity

Statements (19)
Predicate Object
gptkbp:instanceOf gptkb:genetic_disorder
gptkbp:affects integumentary system
skeletal system
gptkbp:firstDescribed 1971
gptkbp:hasGeneticCause mutation in LMNA gene
mutation in ZMPSTE24 gene
gptkbp:hasType type A
type B
gptkbp:inheritance autosomal recessive
gptkbp:OMIM 248370
gptkbp:symptom gptkb:lipodystrophy
skin atrophy
mandibular hypoplasia
acroosteolysis
delayed closure of cranial sutures
gptkbp:synonym gptkb:MAD
gptkbp:bfsParent gptkb:MNDT
gptkbp:bfsLayer 7
https://www.w3.org/2000/01/rdf-schema#label mandibuloacral dysplasia